Adult case of isolated ventricular noncompaction discovered by complete atrioventricular block.

نویسندگان

  • Manabu Taniguchi
  • Toru Hioka
  • Kiyoaki Maekawa
  • Kenji Takagagi
  • Kojiro Shoji
  • Kiyoshi Yoshida
چکیده

A 25-year-old male was admitted to hospital with a 3-day history of worsening faintness. The electrocardiogram showed complete atrioventricular block. Echocardiography showed generalized hypokinesis and prominent trabeculations ranged from the apex to the mid-ventricular lateral wall of the left ventricle as well. Furthermore, trabeculations in the left ventricle were seen in his sister and brother. Thus, isolated ventricular noncompaction (IVNC) was diagnosed and a permanent pacemaker was implanted. Common clinical symptoms of IVNC are heart failure, ventricular arrhythmias, and embolic events. This is the first reported adult case of IVNC disclosed by the presence of complete atrioventricular block.

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عنوان ژورنال:
  • Circulation journal : official journal of the Japanese Circulation Society

دوره 68 9  شماره 

صفحات  -

تاریخ انتشار 2004